Hendriks J J, van de Staak F H, Vio P M, Tolboom J J
Instituut voor Kindergeneeskunde, St. Radboudziekenhuis, K.U. Nijmegen.
Tijdschr Kindergeneeskd. 1989 Feb;57(1):29-31.
A six week old girl with multiple cutaneous haemangiomas and cholestatic jaundice is described. An exploratory laparotomy revealed neither extra- nor intrahepatic biliary atresia. The diagnosis of a diffuse neonatal haemangiomatosis was made. Prednison therapy induced an almost complete normalization of the liverfunction disturbances. Surgical therapy is not the recommended approach for neonatal haemangiomatosis with cholestatic jaundice.
本文描述了一名患有多发性皮肤血管瘤和胆汁淤积性黄疸的六周大女孩。剖腹探查未发现肝外或肝内胆管闭锁。诊断为弥漫性新生儿血管瘤病。泼尼松治疗使肝功能紊乱几乎完全恢复正常。对于患有胆汁淤积性黄疸的新生儿血管瘤病，手术治疗并非推荐的方法。
