Xu Rongjian, Miao Qi, Liu Xingrong, Zhang Chaoji, Ma Guotao
Department of Cardiac Surgery, Peking Union Medical College Hospital, Peking Union Medical College, Chinese Academy of Medical Sciences, Beijing.
Heart Surg Forum. 2016 Apr 4;19(2):E064-6. doi: 10.1532/hsf.1298.
Intravenous leiomyomatosis (IVL) is a rare neoplastic disorder. It may extend into the right cardiac chambers, which are named after intracardiac leiomyomatosis (ICL). We describe a case of IVL extending into the right heart and pulmonary artery in a 46-year-old woman. The patient successfully underwent a one-stage operation under cardiopulmonary bypass (CPB) with deep hypothermic circulatory arrest. The patient fully recovered without major complications and did not exhibit any recurrence at the 9-month follow-up. The unique feature of this case is its involvement with the pulmonary artery, which is uncommon but potentially lethal.
静脉内平滑肌瘤病（IVL）是一种罕见的肿瘤性疾病。它可能延伸至右心腔，这种情况被称为心内平滑肌瘤病（ICL）。我们描述了一例46岁女性的IVL延伸至右心和肺动脉的病例。该患者在体外循环（CPB）及深低温停循环下成功接受了一期手术。患者完全康复，无重大并发症，在9个月的随访中未出现任何复发。该病例的独特之处在于其累及肺动脉，这虽不常见但可能致命。
