Shimada Seijiro, Maekura Shunji, Ino Hikaru, Matsuura Masayosi, Masunaga Nobutaka, Matsumoto Takahiro, Hama Junkichi
Department of Cardiology, Sakai Hospital Kindai University Faculty of Medicine, Japan.
Intern Med. 2016;55(9):1109-15. doi: 10.2169/internalmedicine.55.5835. Epub 2016 May 1.
Amyloidosis is a well-known but uncommon disease, and the physician must maintain a high index of suspicion in order to make a timely diagnosis. The expected survival of patients with cardiac amyloidosis is generally poor. In particular, survival has been reported to be 4-12 months for patients with amyloid light-chain amyloidosis with congestive heart failure. We herein report a rare case of cardiac amyloidosis in which the patient presented with cardiac hypertrophy after a 20-year history of dilated cardiomyopathy and heart failure.
淀粉样变性是一种广为人知但并不常见的疾病，医生必须保持高度的怀疑指数以便及时做出诊断。心脏淀粉样变性患者的预期生存期通常较差。特别是，据报道，患有充血性心力衰竭的轻链淀粉样变性患者的生存期为4至12个月。我们在此报告一例罕见的心脏淀粉样变性病例，该患者在有扩张型心肌病和心力衰竭20年病史后出现心脏肥大。
