扩张型心肌病和心力衰竭病史20年后出现的罕见心脏淀粉样变性病例。

Unusual Case of Cardiac Amyloidosis Preceded by a Twenty-year History of Dilated Cardiomyopathy and Heart Failure.

作者信息

Shimada Seijiro, Maekura Shunji, Ino Hikaru, Matsuura Masayosi, Masunaga Nobutaka, Matsumoto Takahiro, Hama Junkichi

机构信息

Department of Cardiology, Sakai Hospital Kindai University Faculty of Medicine, Japan.

出版信息

Intern Med. 2016;55(9):1109-15. doi: 10.2169/internalmedicine.55.5835. Epub 2016 May 1.

DOI:10.2169/internalmedicine.55.5835

PMID:27150863

Abstract

Amyloidosis is a well-known but uncommon disease, and the physician must maintain a high index of suspicion in order to make a timely diagnosis. The expected survival of patients with cardiac amyloidosis is generally poor. In particular, survival has been reported to be 4-12 months for patients with amyloid light-chain amyloidosis with congestive heart failure. We herein report a rare case of cardiac amyloidosis in which the patient presented with cardiac hypertrophy after a 20-year history of dilated cardiomyopathy and heart failure.

摘要

淀粉样变性是一种广为人知但并不常见的疾病，医生必须保持高度的怀疑指数以便及时做出诊断。心脏淀粉样变性患者的预期生存期通常较差。特别是，据报道，患有充血性心力衰竭的轻链淀粉样变性患者的生存期为4至12个月。我们在此报告一例罕见的心脏淀粉样变性病例，该患者在有扩张型心肌病和心力衰竭20年病史后出现心脏肥大。