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大动脉炎中的中段主动脉综合征:两例手术病例报告。

Middle Aortic Syndrome in Takayasu's Arteritis: Report of Two Surgical Cases.

作者信息

Hinojosa Carlos A, Anaya-Ayala Javier E, Torres-Machorro Adriana, Lizola Rene, Laparra-Escareno Hugo

机构信息

Department of Surgery, Section of Vascular Surgery and Endovascular Therapy, Instituto Nacional de Ciencias Médicas y Nutricion "Salvador Zubirán", Mexico City, Mexico.

Department of Surgery, Section of Vascular Surgery and Endovascular Therapy, Instituto Nacional de Ciencias Médicas y Nutricion "Salvador Zubirán", Mexico City, Mexico.

出版信息

Ann Vasc Surg. 2016 Jul;34:270.e13-7. doi: 10.1016/j.avsg.2015.12.015. Epub 2016 May 10.

DOI:10.1016/j.avsg.2015.12.015
PMID:27174347
Abstract

An isolated stenotic or occluded segment of the descending thoracic and/or the abdominal aorta associated to Takayasu's arteritis (TA) is very uncommon and the clinical expression is known as "middle aortic syndrome." Manifestations depend on the lesion location, and may include hypertension originating from the aortic coarctation or renovascular, buttock, or lower extremity claudication and rarely chronic intestinal angina. We present 2 female patients with TA with occlusive lesions in the infrarenal aorta; both were treated with open surgical reconstruction of the affected segments. On follow-up, at 81 and 46 months, respectively, both patients remain symptoms free.

摘要

与高安动脉炎(TA)相关的降主动脉和/或腹主动脉孤立性狭窄或闭塞段非常罕见,其临床表现被称为“中段主动脉综合征”。临床表现取决于病变部位,可能包括主动脉缩窄或肾血管性高血压、臀部或下肢间歇性跛行,以及罕见的慢性肠绞痛。我们报告2例患有TA且肾下腹主动脉闭塞性病变的女性患者;两名患者均接受了受累节段的开放手术重建。随访时,分别在81个月和46个月时,两名患者均无症状。

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