Bejiqi Ramush, Bejiqi Hana, Retkoceri Ragip
Division of Cardiology, Pediatric Clinic, University Clinical Center of Kosovo, Prishtina, Republic of Kosovo.
Main Center of Family Medicine, Prishtina, Republic of Kosovo.
Open Access Maced J Med Sci. 2016 Mar 15;4(1):74-8. doi: 10.3889/oamjms.2016.016. Epub 2016 Jan 20.
Obstruction to the left ventricular outflow of the heart may be above the aortic valve (5%), at the valve (74%), or in the subvalvar region (23%). These anomalies represent 3 to 6% of all patients with congenital heart defects (CHD), and it occurs more often in males (male-female ratio of 4:1).
The purpose of this study was to determine the sensitivity and specificity of transthoracic echocardiography in diagnosis of discrete subaortic membrane, to determine convenient time for surgical intervention, and for identifying involvement of the aortic valve by subaortic shelf.
A retrospective review of the medical records and echocardiograms of 18 patients [14 male (77%) and 4 female (23%)] with discrete subaortic membrane, aged 11 month to 12 years, with mean age of 5 years and 3 month, diagnosed at the Pediatric Clinic in Prishtina, during the period September, 1999 and December, 2010 were done.
Four patients, in neonatal age were operated from critical coarctation of the aorta and, initial signs of congestive heart failure were presented. 2 of them were operated in Belgrade, Serbia and 2 in Lausanne, Switzerland.
In all presented patients bicuspid aortic valve was noted, but none of them subaortic membrane was registered.
心脏左心室流出道梗阻可能位于主动脉瓣上方（5%）、瓣膜处（74%）或瓣下区域（23%）。这些异常占所有先天性心脏病（CHD）患者的3%至6%，且男性更为常见（男女比例为4:1）。
本研究的目的是确定经胸超声心动图在诊断孤立性主动脉瓣下隔膜中的敏感性和特异性，确定手术干预的合适时机，并识别主动脉瓣下嵴对主动脉瓣的累及情况。
回顾性分析1999年9月至2010年12月期间在普里什蒂纳儿科诊所诊断的18例孤立性主动脉瓣下隔膜患者的病历和超声心动图，患者年龄11个月至12岁，平均年龄5岁3个月，其中男性14例（77%），女性4例（23%）。
4例新生儿因严重主动脉缩窄接受手术，出现充血性心力衰竭的初始症状。其中2例在塞尔维亚贝尔格莱德接受手术，2例在瑞士洛桑接受手术。
在所有呈现的患者中均发现了二叶式主动脉瓣，但均未记录到主动脉瓣下隔膜。
