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采用膀胱外翻一期缝合的泄殖腔外翻修复术:一例病例报告及文献综述

Cloacal Exstrophy Repair with Primary Closure of Bladder Exstrophy: A Case Report and Review of Literature.

作者信息

Bethell George, Johal Navroop, Cuckow Peter

机构信息

Institute of Child Health, University of Liverpool, Liverpool L69 3BX, UK.

Great Ormond Street Children's NHS Trust, Great Ormond Street, London WC1N 3JH, UK.

出版信息

Case Rep Pediatr. 2016;2016:8538935. doi: 10.1155/2016/8538935. Epub 2016 May 23.

DOI:10.1155/2016/8538935
PMID:27313937
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4893573/
Abstract

Cloacal exstrophy is the most complex congenital, ventral, abdominal wall defect. Traditionally surgery consists of a staged approach to repair which takes place on many separate theatre visits. In this case a primary approach was undertaken resulting in a relatively short inpatient stay and a reduced risk from multiple surgical procedures under general anaesthesia.

摘要

泄殖腔外翻是最复杂的先天性腹侧腹壁缺损。传统的手术采用分期修复方法,需要多次在不同的手术台上进行。在这个病例中,采用了一期修复方法,从而使住院时间相对较短,并降低了全身麻醉下多次手术带来的风险。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/842c/4893573/4585d6cff935/CRIPE2016-8538935.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/842c/4893573/6e81527e24d9/CRIPE2016-8538935.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/842c/4893573/4585d6cff935/CRIPE2016-8538935.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/842c/4893573/6e81527e24d9/CRIPE2016-8538935.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/842c/4893573/4585d6cff935/CRIPE2016-8538935.002.jpg

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本文引用的文献

1
Vesico-intestinal Fissure.膀胱肠瘘
Arch Dis Child. 1960 Feb;35(179):97-102. doi: 10.1136/adc.35.179.97.
2
The exstrophy-epispadias complex.尿道上裂-会阴裂畸形。
Orphanet J Rare Dis. 2009 Oct 30;4:23. doi: 10.1186/1750-1172-4-23.
3
Cloacal exstrophy: a comprehensive review of an uncommon problem.先天性直肠会阴瘘:一种罕见问题的全面综述。
J Pediatr Urol. 2010 Apr;6(2):102-11. doi: 10.1016/j.jpurol.2009.09.011. Epub 2009 Oct 23.
4
Can a complete primary repair approach be applied to cloacal exstrophy?完全一期修复方法能否应用于泄殖腔外翻?
J Urol. 2006 Dec;176(6 Pt 1):2643-8. doi: 10.1016/j.juro.2006.08.052.
5
Cloacal exstrophy: a unified management plan.泄殖腔外翻:统一管理方案
J Pediatr Surg. 2000 Jun;35(6):932-7. doi: 10.1053/jpsu.2000.6928.
6
Complete primary repair of exstrophy.膀胱外翻的完全一期修复。
J Urol. 1999 Oct;162(4):1415-20.
7
Cloacal exstrophy: individualized management through a staged surgical approach.泄殖腔外翻:通过分期手术方法进行个体化治疗。
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