Achar Shashidhar Vedavyas, Dutta Hemonta Kumar
Department of Radiodiagnosis, Assam Medical College and Hospital, Dibrugarh, Assam, India.
Department of Pediatric Surgery, Assam Medical College and Hospital, Dibrugarh, Assam, India.
J Clin Imaging Sci. 2016 May 26;6:20. doi: 10.4103/2156-7514.183040. eCollection 2016.
The aim of this study was to evaluate the associated intracranial malformations in patients with sincipital encephaloceles.
A hospital-based cross-sectional study was conducted over 8 years from June 2007 to May 2015 on 28 patients. The patients were evaluated by either computed tomography or magnetic resonance imaging whichever was feasible. Encephaloceles were described with respect to their types, contents, and extensions. A note was made on the associated malformations with sincipital encephaloceles.
Fifty percent of the patients presented before the age of 3 years and both the sexes were affected equally. Nasofrontal encephalocele was the most common type seen in 13 patients (46.4%), and corpus callosal agenesis (12 patients) was the most common associated malformation. Other malformations noted were arachnoid cyst (10 patients), hydrocephalus (7 patients), and agyria-pachygyria complex (2 patients).
Capital Brain malformations are frequently encountered in children with sincipital encephaloceles. Detail radiological evaluation is necessary to plan treatment and also to prognosticate such rare malformations.
本研究旨在评估枕部脑膨出患者伴发的颅内畸形情况。
2007年6月至2015年5月期间，在一家医院开展了一项为期8年的横断面研究，纳入28例患者。根据可行性，对患者采用计算机断层扫描或磁共振成像进行评估。对脑膨出的类型、内容物及延伸情况进行描述，并记录枕部脑膨出伴发的畸形。
50%的患者在3岁前就诊，男女受累情况相同。鼻额部脑膨出是最常见的类型，见于13例患者（46.4%），胼胝体发育不全（12例患者）是最常见的伴发畸形。其他发现的畸形包括蛛网膜囊肿（10例患者）、脑积水（7例患者）以及无脑回-巨脑回复合体（2例患者）。
枕部脑膨出患儿常伴有严重脑畸形。详细的影像学评估对于制定治疗方案以及预测此类罕见畸形很有必要。
