Karadeniz Ümit, Demir Aslı, Koçulu Rabia
Clinic of Anaesthesia, Türkiye Yüksek İhtisas Training and Research Hospital, Ankara, Turkey.
Turk J Anaesthesiol Reanim. 2016 Feb;44(1):50-3. doi: 10.5152/TJAR.2016.91249. Epub 2016 Feb 1.
Long QT syndrome is a congenital disorder that is characterized by a prolongation of the QT interval on electrocardiograms and a propensity to ventricular tachyarrhythmias, which may lead to syncope, cardiac arrest or sudden death. Cardiomyopathy and pulmonary hypertension diseases have additional risks in anaesthesia management. In this study, we emphasize on one lung ventilation, pacemaker-implantable cardioverter-defibrillator and the anaesthesia management process in a patient with long QT syndrome, cardiomyopathy and pulmonary hypertension who underwent thoracic sympathectomy.
长QT综合征是一种先天性疾病,其特征是心电图上QT间期延长以及易发生室性快速心律失常,这可能导致晕厥、心脏骤停或猝死。心肌病和肺动脉高压疾病在麻醉管理中存在额外风险。在本研究中,我们重点关注一名患有长QT综合征、心肌病和肺动脉高压的患者在接受胸交感神经切除术中的单肺通气、可植入式心脏复律除颤器起搏器以及麻醉管理过程。