Gül Enes Elvin, Akdeniz Celal, Tuzcu Volkan
Department of Cardiology, İstanbul Medipol University Faculty of Medicine, İstanbul, Turkey.
Department of Pediatric Cardiology, İstanbul Medipol University Faculty of Medicine, İstanbul, Turkey.
Turk Kardiyol Dern Ars. 2016 Jul;44(5):423-6. doi: 10.5543/tkda.2015.31624.
The atriofascicular accessory pathway (AP), known as the Mahaim pathway, is a rare form of pre-excitation, comprising less than 3% of all APs. Mahaim AP is characterized by decremental, anterograde-only conduction, and antidromic tachycardia with left bundle branch morphology. Prevalence of Mahaim AP in Ebstein's anomaly is significantly high. In addition, combination of Wolff-Parkinson-White (WPW) syndrome and Mahaim AP in patients with Ebstein's anomaly has been reported. Presently described is the coexistence of Mahaim AP and manifest WPW syndrome in a patient with Ebstein's anomaly, who was successfully ablated without fluoroscopy.
房室束旁道(AP),即Mahaim束,是一种罕见的预激形式,在所有AP中占比不到3%。Mahaim束旁道的特点是递减性、仅前向传导,以及具有左束支形态的逆向性心动过速。Mahaim束旁道在埃布斯坦畸形中的患病率显著较高。此外,已有报道称埃布斯坦畸形患者中存在 Wolff-Parkinson-White(WPW)综合征与Mahaim束旁道并存的情况。本文描述了一名埃布斯坦畸形患者中Mahaim束旁道与显性WPW综合征并存的病例,该患者在无透视的情况下成功接受了消融治疗。