Al Sawah Entidhar, Plosker Shayne M, Mikhail Emad
Department of Obstetrics and Gynecology, University of South Florida Morsani College of Medicine, Tampa, Florida.
Surg Technol Int. 2016 Oct 26;29:181-184.
Herlyn-Werner-Wunderlich Syndrome (HWWS) is a rare Müllerian anomaly characterized by uterus didelphys coexisting with an obstructed hemivagina and ipsilateral renal agenesis.
A 13-year-old female presented one-year after menarche with severe dysmenorrhea and a right-sided pelvic mass. Imaging identified a right uterus with hematometra, hematocolpos, absent right kidney, normal left kidney, ureter, left uterus, and vagina compressed to the left by right hematocolpos. We performed laparoscopic hemi-hysterectomy of the non-communicating hemi-uterus, and laparoscopic trachelectomy.
Laparoscopic hemi-hysterectomy and trachelecotmy is a minimally invasive surgical option for patients with Herlyn-Werner-Wunderlich Syndrome.
赫林-韦纳-温德利希综合征（HWWS）是一种罕见的苗勒管异常，其特征为双子宫并存梗阻性半阴道及同侧肾缺如。
一名13岁女性初潮后1年出现严重痛经及右侧盆腔肿块。影像学检查发现右侧子宫积血、阴道积血，右肾缺如，左肾、输尿管、左子宫及阴道正常，右侧阴道积血将阴道向左挤压。我们对不通畅的半侧子宫实施了腹腔镜半子宫切除术及腹腔镜宫颈切除术。
腹腔镜半子宫切除术及宫颈切除术是治疗赫林-韦纳-温德利希综合征患者的一种微创手术选择。
