Van den Bergh P, Logigian E L, Kelly J J
Department of Neurology, Tufts University School of Medicine, New England Medical Center Hospitals, Boston, MA.
Muscle Nerve. 1989 Jan;12(1):26-31. doi: 10.1002/mus.880120106.
We describe a patient with a chronic, symmetric, monophasic, acquired, pure motor, demyelinating polyneuropathy. Electrodiagnostic studies showed the presence of multifocal conduction blocks in motor nerves at sites not prone to compression. A sural nerve biopsy was normal. The patient responded to immunosuppressive therapy and plasma exchange. We postulate that this disorder is an unusual variant of chronic inflammatory polyradiculoneuropathy.
我们描述了一名患有慢性、对称性、单相性、获得性、纯运动性脱髓鞘性多发性神经病的患者。电诊断研究显示,在不易受压部位的运动神经中存在多灶性传导阻滞。腓肠神经活检结果正常。该患者对免疫抑制治疗和血浆置换有反应。我们推测这种疾病是慢性炎症性多发性神经根神经病的一种不寻常变体。