Wu Lin, Wang Ji Mei, Qiao Zhong Wei, Yan Ying Liu, Wang Lai Shuan
Catheterization Laboratory, Children's Hospital of Fudan University, Shanghai, People's Republic of China.
Department of Prenatal Diagnosis Center and Department of Neonatology, Gynecology and Obstetrics Hospital of Fudan University, Shanghai, People's Republic of China.
SAGE Open Med Case Rep. 2015 Nov 3;3:2050313X15615471. doi: 10.1177/2050313X15615471. eCollection 2015.
Congenital hemangioma of the diaphragm is an extremely rare disease in childhood.
We report a newborn presenting with progressive respiratory distress and massive right hydrothorax due to congenital diaphragmatic hemangioma, requiring sustained ventilation support and chest drainage. The angiography revealed that the giant diaphragmatic hemangioma was supplied by the right internal thoracic, inferior diaphragmatic, and intercostal arteries. The selective embolization of the main feeding vessels was successfully achieved using the Embosphere particulates.
The clinical long-term follow-up demonstrated the resolution of the symptoms, pleural effusion, and nearly complete regression of the hemangioma at 18 months of age.
Transcatheter embolization can provide an efficient therapy for symptomatic diaphramatic hemangioma.
先天性膈血管瘤是儿童期一种极其罕见的疾病。
我们报告一例新生儿，因先天性膈血管瘤出现进行性呼吸窘迫和大量右侧胸腔积液，需要持续通气支持和胸腔引流。血管造影显示巨大膈血管瘤由右侧胸廓内动脉、膈下动脉和肋间动脉供血。使用Embosphere微粒成功实现了主要供血血管的选择性栓塞。
临床长期随访显示，18个月大时症状、胸腔积液消失，血管瘤几乎完全消退。
经导管栓塞可为有症状的膈血管瘤提供有效的治疗方法。
