下颌下涎腺髓样肉瘤
Myeloid sarcoma of submandibular salivary gland.
作者信息
Dagna Federico, Giordano Pamela, Boggio Valeria, Albera Roberto
机构信息
ENT Department, A.O.U. Città della Salute e della Scienza di Torino, University of Torino, Torino, Italy.
出版信息
SAGE Open Med Case Rep. 2016 Feb 15;4:2050313X15625016. doi: 10.1177/2050313X15625016. eCollection 2016.
OBJECTIVE
To report a rare case of a myeloid sarcoma of submandibular salivary gland.
METHODS
A 65-year-old woman with a history of successfully treated myelodysplastic syndrome, presenting with periodic painful swelling of her right submandibular area.
RESULTS
Physical evaluation, ultrasound and CT scan revealed the presence of a 3-cm mass contiguous to the submandibular salivary gland. A core needle biopsy confirmed the diagnosis of myeloid sarcoma. Bone marrow biopsy was still showing complete remission and the submandibular gland was the only extramedullary site involved. The patient was submitted to chemotherapy.
CONCLUSION
Myeloid sarcoma is a rare extramedullary neoplasm. It can virtually involve any anatomic site, but it usually involves lymph nodes, paranasal sinuses, skin, soft tissue and periostium. Myeloid sarcomas of salivary glands are very rare and ENTs should be aware of this disease in order to include it in the differential diagnosis of a solitary neck mass.
目的
报告一例罕见的下颌下涎腺髓系肉瘤病例。
方法
一名65岁女性，有骨髓增生异常综合征成功治疗史，出现右侧下颌下区周期性疼痛性肿胀。
结果
体格检查、超声和CT扫描显示下颌下涎腺附近有一个3厘米的肿块。粗针活检确诊为髓系肉瘤。骨髓活检仍显示完全缓解，下颌下腺是唯一受累的髓外部位。患者接受了化疗。
结论
髓系肉瘤是一种罕见的髓外肿瘤。它几乎可累及任何解剖部位，但通常累及淋巴结、鼻窦、皮肤、软组织和骨膜。涎腺髓系肉瘤非常罕见，耳鼻喉科医生应了解这种疾病，以便将其纳入孤立性颈部肿块的鉴别诊断。
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