1型白细胞黏附缺陷症（LAD1），其CD11/CD18表达但无功能。 - Suppr

Leukocyte Adhesion Deficiency Type 1 (LAD1) with Expressed but Nonfunctional CD11/CD18.

作者信息

Cabanillas Diana, Regairaz Lorena, Deswarte Caroline, García Mariel, Richard Marie-Edith, Casanova Jean-Laurent, Bustamante Jacinta, Perez Laura

机构信息

Immunology Unit, Children's Hospital "Superiora Sor María Ludovica", La Plata, Argentina.

Laboratory of Human Genetics of Infectious Diseases, Necker Branch, INSERM U1163, Paris, France.

出版信息

J Clin Immunol. 2016 Oct;36(7):627-30. doi: 10.1007/s10875-016-0322-1. Epub 2016 Aug 4.

DOI:10.1007/s10875-016-0322-1

PMID:27492259

Abstract

摘要

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Leukocyte Adhesion Deficiency Type 1 (LAD1) with Expressed but Nonfunctional CD11/CD18.

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Leukocyte Adhesion Deficiency Type 1 (LAD1) with Expressed but Nonfunctional CD11/CD18.

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