Zhang Chao, Gu Yongquan, Bian Ce, Zhu Guangchang, Luo Tao, Yan Chao, Wang Zhonggao
Department of General Surgery, Xuanwu Hospital, Capital Medical University, Beijing, China.
Department of Vascular Surgery, Xuanwu Hospital, Capital Medical University, Beijing, China.
Ann Vasc Surg. 2017 Jan;38:319.e1-319.e6. doi: 10.1016/j.avsg.2016.05.132. Epub 2016 Aug 20.
Budd-Chiari syndrome (BCS) is a rare hepatic disease caused by occlusion of the hepatic venous outflow at any level from the small hepatic veins to the atriocava junction. BCS could have serious consequences if not treated promptly. The appropriate therapeutic strategy can be offered to change the natural course of the disease. The present case reports a young man with BCS who successfully received the hybrid treatment combined with endovascular intervention and mesocaval shunt by step. The 11-year follow-up showed that the patient was free of clinical symptoms, and computed tomography and ultrasonography confirmed the patency of the stent and shunt. Although BCS therapy methods are well established, the patient often needs to be treated repeatedly because of the high risk of recurrence. Step therapeutic strategy to alleviate portal and inferior vena cava hypertension of BCS patients are respected. The combination of endovascular intervention and mesocaval shunt was effective in our patient, and both stent and shunt have satisfactory long-term patency.
布加综合征(BCS)是一种罕见的肝脏疾病,由从小肝静脉到心房腔静脉交界处任何水平的肝静脉流出道阻塞引起。如果不及时治疗,BCS可能会产生严重后果。可以提供适当的治疗策略来改变疾病的自然进程。本病例报告了一名患有BCS的年轻男性,他成功地接受了血管内介入和肠系膜上腔静脉分流术相结合的分步杂交治疗。11年的随访显示,患者没有临床症状,计算机断层扫描和超声检查证实了支架和分流的通畅。虽然BCS的治疗方法已经很成熟,但由于复发风险高,患者往往需要反复治疗。缓解BCS患者门静脉和下腔静脉高压的分步治疗策略受到重视。血管内介入和肠系膜上腔静脉分流术的联合应用对我们的患者有效,支架和分流都具有令人满意的长期通畅性。