Storozhakov G I, Kopelev A M, Tsareva L A
Ter Arkh. 1989;61(4):135-8.
The authors describe a case of sudden death (SD) of a patient with unaltered coronary arteries, myxomatous degeneration and mitral valve prolapse (MVP). The case was marked by an isolated prolapse of the anterior cusp of the mitral valve because of its congenital structural abnormalities, which was not encountered previously in MVP patients who died suddenly. Microscopic examination showed large-focal cardiosclerosis at the basis of the papillary muscles determined by dysfunction of the mitral apparatus which might be related to the pathogenesis of lethal arrhythmia. It is believed that MVP patients should constitute a separate group with high risk of SD.
作者描述了一例冠状动脉正常、患有黏液瘤样变性和二尖瓣脱垂（MVP）患者的猝死（SD）病例。该病例的特征是二尖瓣前叶因先天性结构异常而孤立脱垂，这在猝死的MVP患者中此前未曾见过。显微镜检查显示，乳头肌基部存在大片局灶性心肌硬化，这是由二尖瓣装置功能障碍所致，可能与致死性心律失常的发病机制有关。据信，MVP患者应构成一个猝死高风险的独立群体。
