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Anesthesia for Complex Cardiovascular Surgery in a Patient With PHACES Syndrome and Review of the Literature.

作者信息

McVey Mark J, Farlinger Chris M, Van Arsdell Glen, Armstrong Derek, Holtby Helen

机构信息

Department of Anesthesia, University of Toronto, Toronto, ON, Canada; Department of Physiology, University of Toronto, Toronto, ON, Canada; Department of Anesthesia and Pain Medicine, The Hospital for Sick Children, Toronto, ON, Canada.

Department of Anesthesia, University of Toronto, Toronto, ON, Canada.

出版信息

J Cardiothorac Vasc Anesth. 2017 Jun;31(3):1042-1047. doi: 10.1053/j.jvca.2016.07.010. Epub 2016 Jul 11.

DOI:10.1053/j.jvca.2016.07.010
PMID:27645824
Abstract
摘要

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2
Moyamoya syndrome and PHACE syndrome: clinical and radiographic characterization of the intracranial arteriopathy and response to surgical revascularization.烟雾综合征和PHACE综合征:颅内动脉病变的临床和影像学特征及对手术血运重建的反应
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Primary repair of complete sternal cleft associated with absent anterior pericardium.与前心包缺如相关的完全性胸骨裂的一期修复。
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Adult presentation of PHACES syndrome.PHACES综合征的成人表现。
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引用本文的文献

1
Preoperative administration of propranolol reduced the surgical risks of PHACES syndrome in a 14-month-old girl.术前给予普萘洛尔降低了一名14个月大女孩患PHACES综合征的手术风险。
BMJ Case Rep. 2019 Apr 29;12(4):e228117. doi: 10.1136/bcr-2018-228117.