Kodeeswaran M, Udesh Reshmi, Ramya L, Jothi Kumar S
Department of Neurosurgery, Government Vellore Medical College and Hospital, Vellore 632011, India
Department of Neurosurgery, Government Vellore Medical College and Hospital, Vellore 632011, India.
J Surg Case Rep. 2016 Sep 20;2016(9):rjw157. doi: 10.1093/jscr/rjw157.
Cavernous angiomas represent 5-12% of all spinal vascular lesions and 1% of all intramedullary lesions in pediatric patients. Intramedullary spinal cavernomas are relatively rare with only 24 cases reported till date to the best of our knowledge. A 15 -year-old boy presented to the clinic with acute onset motor weakness in all four limbs. He was diagnosed with multiple cerebral cavernomas and an acutely bleeding spinal cavernoma. Complete surgical excision of the spinal cavernoma was done. Postoperatively the patient's weakness gradually improved to a power of 4/5 in all his limbs over a period of 10 days. Only 24 cases of pediatric spinal cavernomas have been reported in the current literature. Current consensus on management of these rare lesions is based on previously published case reports/series and surgery appears to be the only definitive treatment. Further studies regarding any non-surgical expectant management appears warranted.
海绵状血管瘤占小儿患者所有脊柱血管病变的5%-12%,占所有髓内病变的1%。脊髓髓内海绵状血管瘤相对罕见,据我们所知,迄今为止仅报道过24例。一名15岁男孩因四肢急性发作性运动无力就诊于诊所。他被诊断为多发性脑海绵状血管瘤和急性出血性脊髓海绵状血管瘤。对脊髓海绵状血管瘤进行了完整的手术切除。术后,患者的无力症状在10天内逐渐改善,四肢肌力恢复至4/5。目前文献中仅报道过24例小儿脊髓海绵状血管瘤。目前对于这些罕见病变的治疗共识基于先前发表的病例报告/系列研究,手术似乎是唯一的确定性治疗方法。关于任何非手术观察治疗的进一步研究似乎很有必要。