Noudel Rémy, Litré Fabien, Vinchon Mathieu, Patey Martine, Rousseaux Pascal
Department of Neurosurgery, Maison Blanche Hospital, University of Reims, Reims, France.
Childs Nerv Syst. 2008 Feb;24(2):259-63. doi: 10.1007/s00381-007-0441-3. Epub 2007 Sep 11.
Intramedullary cavernous angiomas (ImCA) of the spinal cord are very uncommon malformations especially in the pediatric population where only ten cases have yet been reported within the available literature.
In this paper, the authors report the case of a 12-year-old girl presenting with a T11 level hematomyelia because of a cavernous angioma. Microsurgical excision was performed with good clinical outcome and no magnetic resonance imaging evidence of residual cavernoma 30 months later.
Despite the small number of cases reported in children, this one contributes to the literature identifying special features of presentation and management of ImCA for pediatric patients. Because a higher risk of recurrent bleeding has been demonstrated for ImCA, with dramatic clinical consequences, microsurgical removal remains the only definitive treatment.
脊髓髓内海绵状血管瘤(ImCA)是非常罕见的畸形,在儿科人群中尤为如此,现有文献中仅报道了10例。
在本文中,作者报告了一名12岁女孩因海绵状血管瘤导致T11水平脊髓出血性脊髓炎的病例。进行了显微手术切除,临床效果良好,30个月后磁共振成像未显示残留海绵状血管瘤的证据。
尽管儿童中报道的病例数量较少,但该病例为文献提供了有关儿科患者ImCA的特殊表现和治疗特点的信息。由于已证明ImCA有较高的复发出血风险,会产生严重的临床后果,显微手术切除仍然是唯一的确定性治疗方法。