Guerges Mina, Slama Eliza, Maskoni Bashar, Imlay Sherwin, McKany Malik
St. Joseph Mercy Oakland Hospital, 44405 Woodward Ave, Pontiac, MI, 48341, USA.
Ann Med Surg (Lond). 2016 Aug 16;11:16-20. doi: 10.1016/j.amsu.2016.08.004. eCollection 2016 Nov.
Gangliocytic paragangliomas are rare, and typically benign neuroendocrine neoplasms usually found in the second portion of the duodenum. Though recurrence is rare, metastatic cases have been noted. A standardized treatment has not been determined. An endoscopic resection can be carried out, unless metastasis has been noted. We present the case of a patient who underwent an ampullectomy, with successful removal of the tumor, and no recurrence on follow-up.
We present a case involving a 58-year-old gentleman, who presented with dysphagia, and ultimately diagnosed with a periampullary mass proven to be a gangliocytic paraganglioma. The tumor was resected in-toto via an ampullectomy. The patient had no recurrence after twenty-one months.
In conclusion, we present the case of an incidental gangliocytic paraganglioma occurring in the periampullary region of the patient. Ampullectomy was carried out and to date the patient has had no recurrence. Rarity of this tumor, along with treatment choice, makes it especially worthy of notability.
神经节细胞性副神经节瘤罕见，通常是良性神经内分泌肿瘤，多见于十二指肠第二段。虽然复发罕见，但已有转移病例报道。尚未确定标准化治疗方案。除非已发现转移，否则可进行内镜切除。我们报告一例患者，该患者接受了壶腹切除术，成功切除肿瘤，随访无复发。
我们报告一例58岁男性患者，患者因吞咽困难就诊，最终诊断为壶腹周围肿块，经证实为神经节细胞性副神经节瘤。通过壶腹切除术完整切除肿瘤。患者在21个月后无复发。
总之，我们报告了一例发生在患者壶腹周围区域的偶然发现的神经节细胞性副神经节瘤病例。实施了壶腹切除术，迄今为止患者无复发。该肿瘤的罕见性以及治疗选择使其特别值得关注。
