Crim J R, Gold R H, Mirra J M, Eckardt J J, Bassett L W
Department of Radiological Sciences, University of California, Los Angeles, School of Medicine 90024.
Radiology. 1989 Sep;172(3):827-32. doi: 10.1148/radiology.172.3.2772196.
Desmoplastic fibroma (DF) of bone is a rare, nonmetastasizing but locally aggressive tumor that has been discussed infrequently in the radiology literature. The radiographs from 107 previously published cases of DF and seven cases from the authors' institution were analyzed to better understand and define its radiographic characteristics. DF was most common in the mandible, pelvis, and femur. A geographic pattern of bone destruction, with a narrow zone of transition and nonsclerotic margins, was seen in 80 (96%) patients with intraosseous DF for whom radiographs were available (83 patients). Internal pseudotrabeculation was seen in 76 (91%). Although widening of the host bone due to gradual apposition of periosteal new bone was common, occurring in 74 (89%) patients, distinct periosteal new bone occurred in only two (2%) patients with DF of intraosseous origin. The cortex was breached in 23 (28%) patients. Three cases of DF arising in the periosteum were identified and were differentiated radiographically from desmoid tumors of intraosseous or soft-tissue origin.
骨促结缔组织增生性纤维瘤（DF）是一种罕见的、不发生转移但具有局部侵袭性的肿瘤，放射学文献中对其讨论较少。分析了之前发表的107例DF病例的X线片以及作者所在机构的7例病例，以更好地了解和界定其X线特征。DF最常见于下颌骨、骨盆和股骨。在83例有X线片的骨内DF患者中，80例（96%）可见骨质破坏呈地图样，移行带狭窄且边缘无硬化。76例（91%）可见内部假骨小梁形成。虽然由于骨膜新生骨逐渐附着导致宿主骨增宽很常见，74例（89%）患者出现这种情况，但仅2例（2%）骨内源性DF患者出现明显的骨膜新生骨。23例（28%）患者的皮质骨被破坏。确定了3例起源于骨膜的DF病例，并通过放射学方法将其与骨内或软组织起源的硬纤维瘤区分开来。
