Duff C, van Segesser L, Schmid E R, Ziegler W, Turina M
Helv Chir Acta. 1989 Jun;56(1-2):151-3.
Retroperitoneal pheochromocytomas are very uncommon tumors. During the last 10 years only 3 cases have been operated on in our clinic. Two of them were primary retroperitoneal paragangliomas. These two patients are now well and without recurrence 1 and 10 years respectively after operation. The third patient had retroperitoneal metastases of an adrenal pheochromocytoma. Now, after 1 year he has disseminated metastases without response to therapy with (131I)metaiodobenzylguanidine (MIBG). The surgical procedure includes often extended resection and replacement of retroperitoneal blood vessels and requires therefore an experienced surgical team and optimal anesthetic management (Swan-Ganz-katheter). In two cases the aorta was resected and replaced with a Dacron-graft. Reimplantation of both renal arteries into the graft was necessary in one case. Further interventions were: nephrectomy (2x), resection and ligation of the inferior vena cava (1x), resection and replacement of the left renal vein (1x).
腹膜后嗜铬细胞瘤是非常罕见的肿瘤。在过去10年里，我们诊所仅对3例患者进行了手术。其中2例为原发性腹膜后副神经节瘤。这两名患者术后分别已健康存活1年和10年，无复发。第3例患者为肾上腺嗜铬细胞瘤腹膜后转移。现在，1年后他出现了播散性转移，对（131I）间碘苄胍（MIBG）治疗无反应。手术过程通常包括广泛切除和腹膜后血管置换，因此需要经验丰富的手术团队和最佳的麻醉管理（Swan-Ganz导管）。2例患者切除了主动脉并用涤纶移植物进行了置换。1例患者需要将双侧肾动脉重新植入移植物。进一步的干预措施包括：肾切除术（2次）、下腔静脉切除并结扎（1次）、左肾静脉切除并置换（1次）。
