Akcay Murat, Gulel Okan, Soylu Korhan, Meric Murat, Elmali Muzaffer
Cardiology Clinic, Terme State Hospital, Samsun, Turkey.
Department of Cardiology, Faculty of Medicine, Ondokuz Mayis University, Samsun, Turkey.
Rev Port Cardiol. 2016 Dec;35(12):701.e1-701.e3. doi: 10.1016/j.repc.2016.02.008. Epub 2016 Nov 16.
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a rare congenital anomaly characterized by complete or partial aplasia of the uterus and the upper part of the vagina. It is reported to be associated with cardiovascular disorders including atrial septal defect, anomalous pulmonary venous return, aortopulmonary window, pulmonary valve stenosis, mitral valve prolapse, tetralogy of Fallot, truncus arteriosus, and patent ductus arteriosus. Herein, for the first time in the medical literature, we present percutaneous closure of an isolated ostium secundum atrial septal defect in this syndrome.
梅耶-罗基坦斯基-库斯特-豪泽（MRKH）综合征是一种罕见的先天性异常，其特征为子宫和阴道上段完全或部分发育不全。据报道，它与心血管疾病有关，包括房间隔缺损、肺静脉异位回流、主肺动脉窗、肺动脉瓣狭窄、二尖瓣脱垂、法洛四联症、动脉干、动脉导管未闭。在此，我们在医学文献中首次报道了对该综合征中孤立性继发孔房间隔缺损进行经皮封堵术。
