Sözbilen Murat Celal, Günay Hüseyin, Çalış Funda Atamaz
Department of Orthopedics and Traumatology, Medical Faculty of Ege University, 35100 Bornova, İzmir, Turkey.
Eklem Hastalik Cerrahisi. 2016 Dec;27(3):171-4. doi: 10.5606/ehc.2016.34.
Escobar (multiple pterygium) syndrome is progressive and a very rare syndrome. It is generally characterized by multiple pterygia that are found in the cervical, antecubital and popliteal regions. In this report, we present the treatment management of a 14-year-old case with late stage Escobar syndrome who was admitted due to multiple pterygia and bilateral knee contractures. The treatment of this case was conducted in collaboration with the department of orthopedics and the department of physical therapy. The treatment of the case was done in three stages: soft tissue procedures, femoral recurvatum osteotomy and triple arthrodesis, respectively. In addition to all these, the patient did intensive physical therapy for one year. As a result of the operations and physical therapy, adequate muscle strength was obtained.
埃斯科瓦尔（多指（趾）并指（趾）畸形）综合征呈进行性发展，是一种非常罕见的综合征。其一般特征为在颈部、肘前和腘窝区域出现多指（趾）并指（趾）畸形。在本报告中，我们介绍了一名14岁晚期埃斯科瓦尔综合征病例的治疗情况，该患者因多指（趾）并指（趾）畸形和双侧膝关节挛缩入院。该病例的治疗是与骨科和物理治疗科合作进行的。该病例的治疗分三个阶段进行：分别为软组织手术、股骨反屈截骨术和三关节融合术。除此之外，患者还进行了为期一年的强化物理治疗。经过手术和物理治疗，获得了足够的肌肉力量。
