Keren Shay, Dotan Gad, Ben-Cnaan Ran, Leibovitch Leah, Leibovitch Igal
Department of Ophthalmology, Tel Aviv Medical Center, Tel Aviv, Israel; Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.
Department of Ophthalmology, Tel Aviv Medical Center, Tel Aviv, Israel; Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel.
J Plast Reconstr Aesthet Surg. 2017 Mar;70(3):336-340. doi: 10.1016/j.bjps.2016.10.015. Epub 2016 Nov 11.
To describe a series of children with neurofibromatosis type 1 (NF1) and a plexiform neurofibroma of the orbit with ptosis who underwent a combined one-stage surgery for tumor debulking, lid reconstruction, and ptosis repair.
A retrospective review of 6 cases of combined one-step surgeries for orbital plexiform neurofibroma with ptosis.
The study included 6 children (4 boys, mean age 3.4 years). Follow-up time was at least 9 months. All children had unilateral orbitofacial plexiform. All children underwent a combined one-stage surgery performed by a single surgeon for tumor debulking, lid reconstruction, and ptosis repair. There was significant improvement in upper lid height and lid contour postoperatively in all the patients. One patient had early recurrence and underwent another two surgeries in the following years.
A combined surgical approach for orbital involvement in NF1 results in favorable immediate results, though late recurrence may require additional surgical interventions in the future.
描述一系列患有1型神经纤维瘤病（NF1）且患有眼眶丛状神经纤维瘤并伴有上睑下垂的儿童，他们接受了一期联合手术，包括肿瘤减容、眼睑重建和上睑下垂修复。
对6例眼眶丛状神经纤维瘤合并上睑下垂的一期联合手术病例进行回顾性研究。
该研究纳入6名儿童（4名男孩，平均年龄3.4岁）。随访时间至少9个月。所有儿童均为单侧眶面部丛状神经纤维瘤。所有儿童均由同一外科医生进行一期联合手术，包括肿瘤减容、眼睑重建和上睑下垂修复。所有患者术后上睑高度和眼睑轮廓均有显著改善。1例患者早期复发，在随后几年又接受了两次手术。
对于NF1累及眼眶的情况，联合手术方法可取得良好的即刻效果，尽管后期复发可能需要在未来进行额外的手术干预。
