Akbayrak Türkan, Orhan Ceren, Baran Emine, Kaya Serap, Coskun Gürsoy, Varan Ali
Department of Physiotherapy and Rehabilitation, Faculty of Health Sciences, Hacettepe University, Ankara, Turkey.
Division of Pediatric Oncology, Department of Pediatrics, Faculty of Medicine, Hacettepe University, Ankara, Turkey.
Turk J Pediatr. 2016;58(2):203-207. doi: 10.24953/turkjped.2016.02.013.
The aim of the present case report was to investigate the effects of a physiotherapy program combined with sirolimus in a child patient with upper extremity edema and joint limitation due to low-flow vascular malformation. This case report included an 11-year-old male patient (26 kg, 130 cm) diagnosed with congenital lymphovascular malformation on the left and right chest. The patient, who had edema on the upper left extremity and experienced joint limitations, was administered complete decongestive therapy (CDT) and manual therapy in combination with sirolimus. Physiotherapy included a total of 24 sessions, 3 sessions a week for 8 weeks. Following the physiotherapy, the patient was assigned to a home therapy program, and then the maintenance phase of the CDT was initiated. Evaluations were carried out at baseline, at the end of week 8, and after 12 months. Following the physiotherapy program combined with sirolimus, a decrease in extremity volume, an increase in joint movement range, and an improvement in disease-related complaints were observed. Physiotherapy methods combined with sirolimus may be an effective treatment method in patients with vascular malformations. However, further studies with larger sample size are warranted.
本病例报告的目的是研究物理治疗方案联合西罗莫司对一名因低流量血管畸形导致上肢水肿和关节活动受限的儿童患者的影响。本病例报告包括一名11岁男性患者（体重26kg，身高130cm），其左右胸部被诊断为先天性淋巴管血管畸形。该患者左上肢水肿且存在关节活动受限，接受了综合消肿治疗（CDT）、手法治疗并联合使用西罗莫司。物理治疗共进行24次，每周3次，持续8周。物理治疗后，患者被安排进行家庭治疗方案，随后开始CDT的维持阶段。在基线、第8周结束时和12个月后进行评估。在物理治疗方案联合西罗莫司治疗后，观察到肢体体积减小、关节活动范围增加以及与疾病相关的症状有所改善。物理治疗方法联合西罗莫司可能是血管畸形患者的一种有效治疗方法。然而，需要进行更大样本量的进一步研究。
