Saniee Sara, Davarnia Ghazaleh
Department of Dermatology, Tabriz University of Medical Science, Tabriz, Iran.
Case Rep Dermatol. 2016 Nov 21;8(3):327-332. doi: 10.1159/000452319. eCollection 2016 Sep-Dec.
Scleromyxedema is a rare and distinctive variant of cutaneous mucinoses of unknown etiology. It is presenting with generalized papular eruption and sclerodermoid induration. Numerous treatment modalities have been reported to produce partial or permanent responses. This study reports on a case of scleromyxedema without paraproteinemia in a subject who experienced a partial response to thalidomide and prednisolone.
硬化性黏液水肿是一种病因不明的罕见且独特的皮肤黏液病变体。它表现为全身性丘疹性皮疹和硬皮病样硬结。据报道,多种治疗方式可产生部分或永久性疗效。本研究报告了一例无副蛋白血症的硬化性黏液水肿病例,该患者对沙利度胺和泼尼松龙治疗产生了部分疗效。