Lima Mario, Maffi Michela, Gargano Tommaso, Ruggeri Giovanni, Libri Michele, Destro Francesca
Department of Pediatric Surgery, S. Orsola Hospital, University of Bologna, Bologna, Italy.
European J Pediatr Surg Rep. 2016 Dec;4(1):10-12. doi: 10.1055/s-0036-1580705. Epub 2016 Apr 5.
We report the case of a neonate affected by prenatally diagnosed congenital diaphragmatic hernia (CDH), treated by thoracoscopy. During the procedure, we detected an associated extralobar pulmonary sequestration (EPS), which was preoperatively undiagnosed, and we removed it. EPS has been shown to be associated with CDH in up to 15 to 40% of cases. A possible explanation hypothesized is that pulmonary sequestration, which develops at 4 to 5 weeks of gestation, can disturb the fusion of the diaphragm and closure of the pleuroperitoneal canal. The thoracoscopic approach permitted us to identify the thoracic EPS that probably would have been otherwise missed.
我们报告了一例产前诊断为先天性膈疝（CDH）的新生儿病例，该患儿接受了胸腔镜治疗。在手术过程中，我们发现了一个相关的肺叶外隔离症（EPS），术前未被诊断出来，随后将其切除。研究表明，在高达15%至40%的病例中，EPS与CDH有关。一种可能的假设解释是，在妊娠4至5周时发育的肺隔离症可能会干扰膈肌的融合和胸膜腹膜管的闭合。胸腔镜方法使我们能够识别出可能会被遗漏的胸腔内EPS。
