Andrés Peiró José Vicente, Granell Joan Bagó, Moret Montserrat Feliu, Galdó Antonio Moreno
Department of Orthopedic Surgery, Hospital Universitari Vall d'Hebron, Passeig de la Vall d'Hebron 119-129, 08035 Barcelona, Spain.
Department of Orthopedic Surgery, Hospital Universitari Vall d'Hebron, Passeig de la Vall d'Hebron 119-129, 08035 Barcelona, Spain.
Spine Deform. 2017 Jan;5(1):72-76. doi: 10.1016/j.jspd.2016.10.001.
The coexistence of lung disease and scoliosis entails a dramatic situation. There are no papers reporting scoliosis surgery in patients who suffered lung transplantation.
To describe the case of a patient who underwent surgery to correct progressive spinal deformity after two consecutive lung transplants.
Case report, including review of patient records, imaging and pulmonary function tests, and literature review.
A 9-year-old woman diagnosed of idiopathic pulmonary fibrosis and progressive scoliosis underwent lung transplant. Retransplantation of right lung was performed at the age of 14 due to chronic rejection. When she was 16, respiratory function was stable and spinal deformity severely impaired her quality of life. Patient and family demanded a surgical correction. At that moment, she had severe osteoporosis and immunosuppression as a result of anti-rejection therapy. The pattern was a severe double thoracic curve T1-T6 89° and T7-L1 139°. To correct it, a posterior instrumented spine fusion from T2 to L4 using a hybrid configuration was performed.
No significant complications occurred in perioperative, postoperative, and midterm follow-up periods. Solid fusion was achieved and patient was satisfied with surgery. Unfortunately, chronic lung graft rejection worsened her long-term general status.
Scoliosis surgery on lung transplant recipients is feasible, regardless of potential complications related to immunosuppression and osteoporosis. The goal is to improve quality of life.
肺部疾病与脊柱侧凸并存是一种严峻的情况。目前尚无关于肺移植患者进行脊柱侧凸手术的报道。
描述一名在接受两次连续肺移植后接受手术矫正进行性脊柱畸形患者的病例。
病例报告,包括患者记录回顾、影像学和肺功能测试以及文献回顾。
一名9岁女性,诊断为特发性肺纤维化和进行性脊柱侧凸,接受了肺移植。14岁时因慢性排斥反应进行了右肺再次移植。16岁时,呼吸功能稳定,但脊柱畸形严重影响了她的生活质量。患者及其家属要求进行手术矫正。当时,由于抗排斥治疗,她患有严重的骨质疏松症和免疫抑制。畸形表现为严重的双胸弯,T1-T6为89°,T7-L1为139°。为矫正畸形,采用混合构型从T2至L4进行了后路器械辅助脊柱融合术。
围手术期、术后及中期随访期间均未发生明显并发症。实现了坚固融合,患者对手术满意。不幸的是,慢性肺移植排斥反应使她的长期总体状况恶化。
肺移植受者的脊柱侧凸手术是可行的,无论与免疫抑制和骨质疏松相关的潜在并发症如何。目标是改善生活质量。