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作为川崎病的一种罕见并发症,主动脉根部动脉瘤延伸至主动脉弓:外科治疗

Aortic root aneurysm extending into the arch as a rare complication of Kawasaki disease: surgical management.

作者信息

Szalay Zoltan, Papantchev Vassil, Walther Thomas

机构信息

Department of Cardiac Surgery, Kerckhoff Klinik, Bad Nauheim, Germany

出版信息

Eur J Cardiothorac Surg. 2017 Apr 1;51(4):799-801. doi: 10.1093/ejcts/ezw379.

Abstract

An aortic aneurysm complicating Kawasaki disease (KD) is extremely rare. We herein report a case of 48-year-old KD patient with severe aortic regurgitation, aneurysm of the aortic root, ascending aorta and aortic arch, and giant heavily calcified coronary aneurysms. The patient underwent successful surgical management. This case raises some unusual technical issues, which are discussed. A review of the literature is also offered.

摘要

川崎病(KD)合并主动脉瘤极为罕见。我们在此报告一例48岁的KD患者,该患者患有严重主动脉瓣反流、主动脉根部、升主动脉和主动脉弓动脉瘤以及巨大且重度钙化的冠状动脉瘤。该患者接受了成功的手术治疗。本病例引发了一些特殊的技术问题,对此进行了讨论。同时也提供了文献综述。

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