Neural Stem Cells Laboratory, Institute of Medical Biology, 138648 Singapore.
Epithelial Epigenetics and Development Laboratory, Institute of Medical Biology, 138648 Singapore.
Sci Rep. 2017 Jan 9;7:40485. doi: 10.1038/srep40485.
The insulin receptor substrate of 53 kDa, IRSp53, is an adaptor protein that works with activated GTPases, Cdc42 and Rac, to modulate actin dynamics and generate membrane protrusions in response to cell signaling. Adult mice that lack IRSp53 fail to regulate synaptic plasticity and exhibit hippocampus-associated learning deficiencies. Here, we show that 60% of IRSp53 null embryos die at mid to late gestation, indicating a vital IRSp53 function in embryonic development. We find that IRSp53 KO embryos displayed pleiotropic phenotypes such as developmental delay, oligodactyly and subcutaneous edema, and died of severely impaired cardiac and placental development. We further show that double knockout of IRSp53 and its closest family member, IRTKS, resulted in exacerbated placental abnormalities, particularly in spongiotrophoblast differentiation and development, giving rise to complete embryonic lethality. Hence, our findings demonstrate a hitherto under-appreciated IRSp53 function in embryonic development, and further establish an essential genetic interaction between IRSp53 and IRTKS in placental formation.
53kDa 的胰岛素受体底物(IRSp53)是一种衔接蛋白,它与激活的 GTP 酶(Cdc42 和 Rac)一起作用,调节肌动蛋白动力学,并在细胞信号转导过程中产生膜突。缺乏 IRSp53 的成年小鼠无法调节突触可塑性,并表现出与海马体相关的学习缺陷。在这里,我们表明,60%的 IRSp53 缺失胚胎在中期至晚期妊娠时死亡,这表明 IRSp53 在胚胎发育中具有重要功能。我们发现,IRSp53 KO 胚胎表现出多种表型,如发育迟缓、少指(趾)畸形和皮下水肿,并因严重的心脏和胎盘发育不良而死亡。我们进一步表明,IRSp53 和其最接近的家族成员 IRTKS 的双敲除导致胎盘异常加剧,特别是在海绵滋养层分化和发育方面,导致完全胚胎致死。因此,我们的研究结果表明了 IRSp53 在胚胎发育中的一个以前未被充分认识的功能,并进一步证实了 IRSp53 和 IRTKS 在胎盘形成中的重要遗传相互作用。