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Tracheal agenesis with bronchoesophageal fistulas--a case report.

作者信息

Nakada K, Kitagawa H, Enami T, Yamate N, Tsukada K, Seki I

机构信息

Third Department of Surgery, St. Marianna University School of Medicine, Kawasaki, Japan.

出版信息

Jpn J Surg. 1989 Jul;19(4):494-7. doi: 10.1007/BF02471635.

DOI:10.1007/BF02471635
PMID:2810963
Abstract

Although tracheal agenesis is presently considered to be a rare and fatal anomaly, an increasing number of institutions have been reporting such cases. Reported herein, is a clinical and necropsy report of a premature infant whose tracheal agenesis was associated with broncho-esophageal fistulas and an imperforate anus. Accidental esophageal intubation enabled a perineal anoplasty to be performed under general anesthesia and allowed him to survive for 14 days.

摘要

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本文引用的文献

1
Surgical treatment of tracheal agenesis.
J Thorac Cardiovasc Surg. 1963 Apr;45:520-5.
2
Agenesis of the trachea.气管缺如
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Tracheal agenesis: a clinical approach.气管闭锁:临床诊治方法
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Tracheal agenesis.气管闭锁
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J Pediatr Surg. 1972 Apr;7(2):112-8. doi: 10.1016/0022-3468(72)90483-6.
7
Tracheal agenesis with broncho-esophageal fistula.
Laryngoscope. 1973 Feb;83(2):250-4. doi: 10.1288/00005537-197302000-00006.
8
Tracheal agenesis and associated malformations: a comparison with tracheoesophageal fistula and the VACTERL association.气管发育不全及相关畸形:与气管食管瘘和VACTERL综合征的比较
Am J Med Genet. 1985 May;21(1):21-38. doi: 10.1002/ajmg.1320210104.