Oliver Edward R, Coleman Beverly G, DeBari Suzanne E, Victoria Teresa, Looney Devon M, Horii Steven C, Moldenhauer Julie S, Langer Jill E, Howell Lori J, Pawel Bruce R, Adzick N Scott
Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, USA.
Center for Fetal Diagnosis and Treatment, Children's Hospital of Philadelphia, Philadelphia, Pennsylvania, USA.
J Ultrasound Med. 2017 May;36(5):1051-1058. doi: 10.7863/ultra.16.04071. Epub 2017 Jan 27.
Lymphatic malformations are benign lesions that result from abnormal development of the lymphatic and venous systems. These lesions may be detected during routine prenatal ultrasound screening, and typically demonstrate imaging findings of a multiseptate cystic lesion lacking solid components, vascularity, and calcifications. We report 73 cases of prenatally detected lymphatic malformations and describe greater variability in their prenatal sonographic appearance than previously reported, including purely cystic lesions and mixed cystic and solid lesions with calcifications. Appreciation of this increased variability is important in providing accurate prenatal diagnosis, counseling, and management.
淋巴管畸形是由淋巴系统和静脉系统发育异常导致的良性病变。这些病变可能在常规产前超声筛查时被发现,通常表现为多房性囊性病变,缺乏实性成分、血管和钙化的影像学特征。我们报告了73例产前检测到的淋巴管畸形病例,并描述了其产前超声表现比先前报道的有更大的变异性,包括单纯囊性病变以及伴有钙化的囊性和实性混合病变。认识到这种增加的变异性对于提供准确的产前诊断、咨询和管理非常重要。