Alkhulaifat Dana, Ramirez-Suarez Karen I, Otero Hansel J, Rapp Jordan B, Srinivasan Abhay S, Smith Christopher L, Biko David M
Department of Radiology, Children's Hospital of Philadelphia, Philadelphia, PA, USA.
Perelman School of Medicine at The University of Pennsylvania, Philadelphia, PA, USA.
Pediatr Radiol. 2025 Jan 24. doi: 10.1007/s00247-025-06167-9.
Complex lymphatic anomalies are unique diseases marked by abnormal lymphatic vessel development and growth. Imaging is crucial in the evaluation and management of complex lymphatic anomalies, with dynamic contrast-enhanced MR lymphangiography emerging as a valuable modality for visualizing abnormal lymphatic structures and informing treatment decisions. This article gives an overview of complex lymphatic anomalies and their management strategies, focusing specifically on generalized lymphatic anomaly, Gorham-Stout disease, Kaposiform lymphangiomatosis, and central conducting lymphatic anomalies. Simple lymphatic diseases are beyond the scope of this review.
复杂性淋巴管畸形是一类独特的疾病，其特征为淋巴管发育和生长异常。影像学检查在复杂性淋巴管畸形的评估和管理中至关重要，动态对比增强磁共振淋巴管造影已成为一种有价值的检查方式，可用于显示异常淋巴管结构并为治疗决策提供依据。本文概述了复杂性淋巴管畸形及其管理策略，特别聚焦于泛发性淋巴管畸形、戈谢病、卡波西样淋巴管瘤病和中央传导性淋巴管畸形。单纯性淋巴管疾病不在本综述范围内。
