Ohtake Reiko, Yamaguchi Tsuyoshi, Murata Satoshi, Kaida Sachiko, Yamamoto Hiroshi, Takebayashi Katsushi, Akabori Hiroya, Sonoda Hiromichi, Mori Tsuyoshi, Shimizu Tomoharu, Naka Shigeyuki, Banba Shigeki, Tsujikawa Tomoyuki, Ando Akira, Tani Masaji
Dept. of Surgery, Shiga University of Medical Science.
Gan To Kagaku Ryoho. 2016 Nov;43(12):1687-1689.
We report 3 cases of multiple GIST of the small intestine in 3 patients with NF1 who have been followed for over 5 years. All patients presented with melena, and tumors of the small intestine suspected to be GIST were found on endoscopy. We performed partial resections of the small intestine for all 3 patients. After surgery, 1 patient had residual tumors that gradually enlarged during 8 year 2 months and another had residual tumors that have been stable for 8 years. In the third patient, we resected all the tumors, and there has been no sign of recurrence in 6 year 1 month.
我们报告了3例患有1型神经纤维瘤病（NF1）且随访超过5年的小肠多发胃肠道间质瘤（GIST）患者。所有患者均表现为黑便，内镜检查发现小肠有疑似GIST的肿瘤。我们对所有3例患者均进行了小肠部分切除术。术后，1例患者有残留肿瘤，在8年2个月期间逐渐增大，另1例患者的残留肿瘤已稳定8年。在第3例患者中，我们切除了所有肿瘤，6年1个月来未见复发迹象。
