Endo Hitoshi, Ohno Makoto, Kobayashi Toshiya
Department of Cardiovascular Surgery, St. Marianna University School of Medicine, Yokohama City Seibu Hospital, Yokohama, Japan.
Kyobu Geka. 2017 Feb;70(2):131-134.
Primary tumors of the heart are rare. In the literature operations for heart tumors account for 0.3% of all cardiac surgical procedures. We report a very rare case of primary cardiac angiomyolipoma. A 39-years-old man was admitted with chest discomfort. A mass was detected in the left ventricular myocardium by enhanced chest computed tomography. We performed resection of the intramyocardial tumor under cardiopulmonary bypass. Pathologic examination revealed a 4×3×3 cm, dome-shaped, solid tumor composed of a mixture of blood vessels, smooth muscle, and fat tissue. Histopathological findings showed that the tumor was angiomyolipoma. Angiomyolipoma is a benign tumor and usually develop in the kidney and are associated with tuberous sclerosis. In our case, there was no evidence of tuberous sclerosis.
原发性心脏肿瘤很罕见。文献报道心脏肿瘤手术占所有心脏外科手术的0.3%。我们报告一例非常罕见的原发性心脏血管平滑肌脂肪瘤病例。一名39岁男性因胸部不适入院。胸部增强计算机断层扫描在左心室心肌中检测到一个肿块。我们在体外循环下对心肌内肿瘤进行了切除。病理检查显示为一个4×3×3厘米、圆顶状的实性肿瘤，由血管、平滑肌和脂肪组织混合组成。组织病理学检查结果显示该肿瘤为血管平滑肌脂肪瘤。血管平滑肌脂肪瘤是一种良性肿瘤，通常发生在肾脏，与结节性硬化症有关。在我们的病例中，没有结节性硬化症的证据。
