马凡综合征患者出现升主动脉瘤和膈疝。
Ascending aortic aneurysm and diaphragmatic hernia in a case of Marfan syndrome.
作者信息
Kothari Jignesh, Hinduja Manish, Baria Kinnaresh, Pandya Himani
机构信息
UN Mehta Institute of Cardiology and Research Center (affiliated to BJ Medical College), Ahmedabad, India.
出版信息
Asian Cardiovasc Thorac Ann. 2017 Jun;25(5):378-380. doi: 10.1177/0218492317693694. Epub 2017 Feb 10.
Marfan syndrome commonly affects the skeletal, ocular, and cardiovascular systems. Involvement of the gastrointestinal system is known but uncommon. Intervention depends upon the system involved and the severity of symptoms. Special awareness is required for the diagnosis and management of gastrointestinal involvement in these patients. We report a rare case of simultaneous surgical repair of an ascending aortic aneurysm and a type IV hiatal hernia in a 35-year-old man with Marfan syndrome.
马凡综合征通常影响骨骼、眼睛和心血管系统。胃肠道系统受累虽已为人所知，但并不常见。干预措施取决于受累系统及症状的严重程度。对于这些患者胃肠道受累的诊断和管理需要特别关注。我们报告一例罕见病例，一名35岁患有马凡综合征的男性同时接受了升主动脉瘤和IV型食管裂孔疝的手术修复。
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