Uçar Mustafa Gazi, Ilhan Tolgay Tuyan, Gül Ayhan, Ugurluoglu Ceyhan, Çelik Çetin
Assistant Professor, Department of Obstetrics and Gynaecology, Selçuk University Medicine Faculty , Selçuklu, Konya, Turkey .
Assistant Professor, Faculty, Department of Pathology, Selçuk University Medicine Faculty , Selçuklu, Konya, Turkey .
J Clin Diagn Res. 2016 Dec;10(12):QD05-QD07. doi: 10.7860/JCDR/2016/22152.9061. Epub 2016 Dec 1.
Uterine Tumour Resembling Ovarian Sex-Cord Tumours (UTROSCTs) are an extremely rare type of uterine body tumours arising from the endometrial stroma. Epidemiology, aetiology, pathogenesis, management and natural history of UTROSCTs are still a question of debate, as there is little available data in the literature. Although rare, the possibility of UTROSCTs should be kept in mind, when a patient presents with abnormal bleeding and an enlarged uterus. UTROSCTs appear dirty white/cream-coloured, gelatinous, well-circumscribed mass with smooth surface on macroscopic examination. We present a rare case of endometrial stromal tumour with sex-cord-like differentiation which was successfully treated by hysterectomy with bilateral salpingo-oophorectomy. The clinical manifestations, pathologic characteristics, diagnosis and management of these tumours are reviewed here.
子宫肿瘤样卵巢性索肿瘤（UTROSCTs）是一种极其罕见的起源于子宫内膜间质的子宫体肿瘤。UTROSCTs的流行病学、病因学、发病机制、治疗及自然史仍是一个有争议的问题，因为文献中可用的数据很少。尽管罕见，但当患者出现异常出血和子宫增大时，应考虑UTROSCTs的可能性。UTROSCTs在宏观检查时表现为灰白色/米色、胶冻状、边界清晰、表面光滑的肿块。我们报告一例罕见的具有性索样分化的子宫内膜间质肿瘤，通过子宫切除术加双侧输卵管卵巢切除术成功治疗。本文对这些肿瘤的临床表现、病理特征、诊断和治疗进行了综述。
