Wilhelm K R, Lenarz T, Weise D, Baldauf G, Fritz P, Bihl H
Nuklearmedizinische Abteilung der Universitäts-Strahlenklinik Heidelberg.
Rofo. 1987 Sep;147(3):278-82. doi: 10.1055/s-2008-1048639.
Camurati-Engelmann disease is a rare progressive bone dysplasia; involvement of the skull base can lead to deafness, vestibular disturbances, facial paralysis and damage to the optic nerves. Treatment with corticosteroids, calcitonin and diphosphonates promises only very limited success. Conservative treatment of compression of the cranial nerves is almost ineffective, but the aim of surgical treatment is decompression of involved nerves. The differential diagnosis depends on radiological findings and clinical symptoms. Follow-up depends on radiographic examination and skeletal scintigraphy for showing the extent of the disease. CT may help in demonstrating compression of cranial nerves and define the indications for surgical decompression.
