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右胸腹联合入路用于心脏后副神经节瘤切除术

Right Thoracoabdominal Approach for Retrocardiac Paraganglioma Resection.

作者信息

Hinojosa Carlos A, Laparra-Escareno Hugo, Anaya-Ayala Javier E, Lizola Rene, Torres-Machorro Adriana, Gamboa-Domínguez Armando

出版信息

Tex Heart Inst J. 2017 Feb 1;44(1):62-65. doi: 10.14503/THIJ-15-5561. eCollection 2017 Feb.

Abstract

Paragangliomas are rare extra-adrenal tumors of sympathetic or parasympathetic paraganglia origin; of these, mediastinal paragangliomas are 2% of all cases. We present the case of a 21-year-old woman with uncontrolled arterial hypertension who had a functioning 6.5 × 6.2-cm retrocardiac paraganglioma firmly attached to the pericardium. The patient underwent tumor resection via a right thoracoabdominal incision; this surgical approach enabled adequate exposure for complete resection without institution of cardiopulmonary bypass or need for cardiac reconstruction or autotransplantation. Ten months postoperatively, the patient was doing well and was no longer hypertensive.

摘要

副神经节瘤是起源于交感或副交感神经节的罕见肾上腺外肿瘤;其中,纵隔副神经节瘤占所有病例的2%。我们报告了一例21岁女性病例,该患者患有无法控制的动脉高血压,其心脏后方有一个6.5×6.2厘米大小、有功能的副神经节瘤,与心包紧密相连。患者通过右胸腹联合切口进行肿瘤切除;这种手术方法能够充分暴露肿瘤以进行完整切除,无需进行体外循环,也无需进行心脏重建或自体移植。术后十个月,患者情况良好,不再患有高血压。

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