Harky Amer, Bashir Mohamad, Garner Megan, Hsia TainYen
Department of Cardiothoracic Surgery, Barts Heart Centre, St Bartholomew's Hospital, London, UK.
Barts Heart Centre, St Bartholomew's Hospital, London, UK.
BMJ Case Rep. 2017 Mar 9;2017:bcr2016219184. doi: 10.1136/bcr-2016-219184.
We report a case of an incidental finding of an anomalous left circumflex coronary artery arising from the right pulmonary artery that effectuated a ventricular fibrillation cardiac arrest in a woman aged 34 years. This rarity was detected during routine work-up to delineate the cause of this arrhythmia. Our patient had a background of double-outlet right ventricle and a ventricular septal defect, which was repaired with a Dacron patch and a left ventricle patch over to the aorta at age 14 months. Angiographic study at the time of her presentation showed anomalous origin of the left circumflex artery originating from the right pulmonary artery; this was discussed in multispecialty team meeting and surgical intervention was recommended; eventually, surgery was performed with reimplantation of the anomalous circumflex artery into the ascending aorta. We highlight the importance of early angiographic studies in patients with known congenital heart defects and emphasise the optimal strategy of treatment.
我们报告了一例34岁女性患者,其在常规检查中偶然发现左旋支冠状动脉起源异常,发自右肺动脉,进而引发心室颤动心脏骤停。这种罕见情况是在为明确该心律失常病因的常规检查过程中被发现的。我们的患者有双出口右心室和室间隔缺损病史,在14个月大时使用涤纶补片和左心室补片进行了修复,将左心室补片覆盖至主动脉。她就诊时的血管造影研究显示左旋支动脉起源异常,发自右肺动脉;多学科团队会议对此进行了讨论,并建议进行手术干预;最终,通过将异常的左旋支动脉重新植入升主动脉进行了手术。我们强调了对已知先天性心脏缺陷患者进行早期血管造影研究的重要性,并强调了最佳治疗策略。