Catovsky D, O'Brien M, Cherchi M, Benavides I
Boll Ist Sieroter Milan. 1978 Jul 31;57(3):344-54.
The blast cells of 19 patients with Ph1-positive chronic granulocytic leukaemia (CGL) in blast crisis (BC) were studied by means of several techniques: morphology, cytochemistry, ultrastructure, surface markers and the enzyme terminal transferase. Cells of BC were, in most case, extremely undifferentiated by morphology and cytochemistry. Our data showed that in 80% of cases the cells in BC were myeloid and in 20% they were "lymphoblastic". The M1, M2 and M3 forms (FAB classification) were rare in CGL BC compared with acute myeloid leukaemia (AML). A megakaryoblastic type was seen in 15% of BC cases; the existence of this form could only be demonstrated by electron microscopy. The limphoblastic BC cells were, as in acute lymphoblastic leukaemia (ALL), positive with Greaves' anti-ALL serum and had elevated levels of terminal transferase. A case of a 17-year old boy presenting as ALL, reverting to chronic-phase CGL after complete remission and developing terminally a myeloid BC is described in detail. This case helps to illustrate a new form of natural history of CGL unveiled by the present study.
采用多种技术对19例处于急变期(BC)的Ph1阳性慢性粒细胞白血病(CGL)患者的原始细胞进行了研究:形态学、细胞化学、超微结构、表面标志物以及末端转移酶。多数情况下,急变期细胞在形态学和细胞化学上极不分化。我们的数据显示,80%的急变期病例细胞为髓系,20%为“淋巴母细胞性”。与急性髓细胞白血病(AML)相比,CGL急变期的M1、M2和M3型(FAB分类)较为少见。15%的急变期病例可见巨核母细胞型;这种类型的存在只能通过电子显微镜证实。淋巴母细胞性急变期细胞与急性淋巴细胞白血病(ALL)一样,对格里夫斯抗ALL血清呈阳性反应,且末端转移酶水平升高。详细描述了1例17岁男孩,初诊为ALL,完全缓解后转变为慢性期CGL,最终发展为髓系急变期的病例。该病例有助于说明本研究揭示的CGL自然史的一种新形式。