Skakkebæk Anne, Moore Philip J, Pedersen Anders Degn, Bojesen Anders, Kristensen Maria Krarup, Fedder Jens, Laurberg Peter, Hertz Jens Michael, Østergaard John Rosendahl, Wallentin Mikkel, Gravholt Claus Højbjerg
Department of Endocrinology and Internal Medicine (MEA) Aarhus University Hospital Aarhus Denmark; Department of Clinical Genetics Aarhus University Hospital Aarhus Denmark.
Department of Psychology The George Washington University Washington DC USA.
Brain Behav. 2017 Feb 9;7(3):e00645. doi: 10.1002/brb3.645. eCollection 2017 Mar.
The determinants of cognitive deficits among individuals with Klinefelter syndrome (KS) are not well understood. This study was conducted to assess the impact of general intelligence, personality, and social engagement on cognitive performance among patients with KS and a group of controls matched for age and years of education.
Sixty-nine patients with KS and 69 controls were assessed in terms of IQ, NEO personality inventory, the Autism Spectrum Quotient (AQ) scale, and measures of cognitive performance reflecting working memory and executive function.
Patients with KS performed more poorly on memory and executive-function tasks. Patients with KS also exhibited greater neuroticism and less extraversion, openness, and conscientiousness than controls. Memory deficits among patients with KS were associated with lower intelligence, while diminished executive functioning was mediated by both lower intelligence and less social engagement.
Our results suggest that among patients with KS, memory deficits are principally a function of lower general intelligence, while executive-function deficits are associated with both lower intelligence and poorer social skills. This suggests a potential influence of social engagement on executive cognitive functioning (and/or vice-versa) among individuals with KS, and perhaps those with other genetic disorders. Future longitudinal research would be important to further clarify this and other issues discussed in this research.
克氏综合征(KS)患者认知缺陷的决定因素尚未得到充分理解。本研究旨在评估一般智力、人格和社会参与度对KS患者以及一组年龄和受教育年限匹配的对照组患者认知表现的影响。
对69例KS患者和69例对照者进行了智商、大五人格量表、自闭症谱系商数(AQ)量表评估,以及反映工作记忆和执行功能的认知表现测量。
KS患者在记忆和执行功能任务上表现更差。与对照组相比,KS患者还表现出更高的神经质,以及更低的外向性、开放性和尽责性。KS患者的记忆缺陷与较低的智力相关,而执行功能的减退则由较低的智力和较少的社会参与共同介导。
我们的结果表明,在KS患者中,记忆缺陷主要是一般智力较低的结果,而执行功能缺陷则与较低的智力和较差的社交技能有关。这表明社会参与度可能对KS患者(或许还有其他遗传性疾病患者)的执行认知功能有潜在影响(反之亦然)。未来的纵向研究对于进一步阐明本研究中讨论的这一问题及其他问题将具有重要意义。