Gulzar Rubina, Shahid Ruqaiya, Mirza Talat
Department of Pathology, Dow International Medical College, Dow Diagnostic Research and Reference Laboratory, Dow University of Health Sciences, Karachi.
J Coll Physicians Surg Pak. 2017 Mar;27(3):S61-S62.
Teratoma is a rare tumor, containing structures originating from all three germinal layers. The most frequent location of teratoma is the gonads. Orbital teratoma is extremely rare. In 1969, Jensen reported that only 40 cases of orbital teratoma existed in the world. We describe a rare case of orbital teratoma in a 15-day girl who presented with marked proptosis of the left eye. The eyeball was embedded within the mass that could be seen all around the globe. Orbitectomy was performed with the impression of retinoblastoma. Histopathological examination was reported as benign mature cystic teratoma; no immature component was identified. The case is being reported because of its rarity and also to highlight the use of modern neuroimaging techniques in making an accurate preoperative diagnosis, which helps in better operative management of these patients.
畸胎瘤是一种罕见肿瘤，包含源自所有三个胚层的结构。畸胎瘤最常见的部位是性腺。眼眶畸胎瘤极为罕见。1969年，詹森报告称世界上仅有40例眼眶畸胎瘤病例。我们描述了一例15天大女童眼眶畸胎瘤的罕见病例，该女童表现为左眼明显突出。眼球嵌于可在眼球周围各处看到的肿块内。因怀疑视网膜母细胞瘤而进行了眶切除术。组织病理学检查报告为良性成熟囊性畸胎瘤；未发现不成熟成分。报告该病例是因其罕见性，同时也是为了强调现代神经影像技术在进行准确术前诊断中的应用，这有助于对这些患者进行更好的手术管理。
