Branco Cláudio, Vilaça Sónia, Falcão Joaquim
Department of General Surgery, Hospital of Braga, Braga, Portugal.
Department of General Surgery, Hospital of Braga, Braga, Portugal.
Int J Surg Case Rep. 2017;33:148-150. doi: 10.1016/j.ijscr.2017.02.049. Epub 2017 Feb 28.
Solid pseudopapillary neoplasm (SPN) is a rare pancreatic tumor. Most patients are female within the second or third decade of life with only a small minority concerning children. Frequently described as low malignant potential tumors, surgical resection remains the main treatment.
The authors present a case of a SPN diagnosed in a 17-year-old Caucasian girl with vomiting and abdominal pain localized to the right upper quadrant. CT scans and MRI scans showed the presence of a well-defined tumor arising from the pancreatic head with 14cm of greater diameter. Pylorus-preserving pancreatoduodenectomy was performed and histopathology confirmed a SPN with complete resection and no evidence of malignancy.
SPN are usually found incidentally hence the importance of an accurate radiologic diagnosis. Symptoms may be present such as abdominal pain or vomiting due to compression, namely in large tumors. A surgical approach is usually indicated aiming complete resection, with tumor size not predicting resectability.
Solid pseudopapillary tumors of the pancreas are extremely rare and usually have an excellent long-term prognosis after surgical resection.
实性假乳头状肿瘤（SPN）是一种罕见的胰腺肿瘤。大多数患者为二三十岁的女性，只有极少数是儿童。SPN常被描述为具有低恶性潜能的肿瘤，手术切除仍是主要治疗方法。
作者报告一例17岁白种女孩诊断为SPN的病例，该女孩有呕吐症状，腹痛位于右上腹。CT扫描和MRI扫描显示胰头部有一个边界清晰的肿瘤，直径大于14厘米。实施了保留幽门的胰十二指肠切除术，组织病理学证实为SPN，肿瘤完整切除，无恶性证据。
SPN通常是偶然发现的，因此准确的放射学诊断很重要。可能会出现症状，如因肿瘤压迫引起的腹痛或呕吐，尤其是在肿瘤较大时。通常需要采取手术方法以实现完整切除，肿瘤大小并不能预测可切除性。
胰腺实性假乳头状肿瘤极为罕见，手术切除后通常具有良好的长期预后。
