Michotte A, Dierckx R, Deleu D, Herregodts P, Schmedding E, Bruyland M, Ebinger G
Department of Neurology, University Hospital A.Z.V.U.B., Belgium.
Clin Neurol Neurosurg. 1988;90(1):71-4. doi: 10.1016/s0303-8467(88)80014-3.
Two patients presenting a relapsing form of sporadic brachial plexus neuropathy, the so-called Parsonage Turner syndrome, are reported. The diagnosis is based on clinical and electromyographic features. Recurrent attacks, although infrequently encountered, have been well described in the past. Sporadic cases of this syndrome must be differentiated from the familial varieties of neuralgic amyotrophy in which, two main subgroups of patients are distinguished: those showing facial dysmorphic features and those with findings of a tomaculous neuropathy predisposing them to pressure palsies. Apart from the obvious difference as regards familial occurrence, the familial and non-familial varieties of neuralgic amyotrophy differ in a number of respects: associated congenital defects, early age of onset and high rate of recurrence in the former. Finally some possible pathogenetic mechanisms of the syndrome are briefly reviewed.
本文报告了两名表现为散发性臂丛神经病复发形式(即所谓的帕森奇-特纳综合征)的患者。诊断基于临床和肌电图特征。复发发作虽不常见,但过去已有详细描述。该综合征的散发病例必须与神经痛性肌萎缩的家族性类型相鉴别,后者可分为两个主要亚组:表现出面部畸形特征的患者和有腊肠样神经病表现且易患压迫性麻痹的患者。除了家族性发病这一明显差异外,神经痛性肌萎缩的家族性和非家族性类型在多个方面存在不同:前者伴有先天性缺陷、发病年龄早且复发率高。最后简要回顾了该综合征一些可能的发病机制。