Kawecki Damian, Dola Janusz, Jacheć Wojciech, Wojciechowska Celina, Morawski Stanisław, Tomasik Andrzej, Nowalany-Kozielska Ewa
2 Department of Cardiology in Zabrze, Medical University of Silesia in Katowice, Sklodowskiej-Curie 10 Street, 41-800 Zabrze, Poland.
2 Department of Cardiology in Zabrze, Medical University of Silesia in Katowice, Sklodowskiej-Curie 10 Street, 41-800 Zabrze, Poland, Tel: +48 32 271 10 10;
Open Med (Wars). 2015 Jan 15;10(1):113-118. doi: 10.1515/med-2015-0023. eCollection 2015.
Long QT syndrome (LQTS) is characterised by both the depolarisation and repolarisation disorder of cardiac muscle cells. Cardiac resynchronising therapy (CRT) is an important treatment option for patients with chronic heart failure (CHF) when echocardiographic and electrocardiographic criteria are met. Although CRT was introduced in clinical practice 10 years ago, doubts related to application of this treatment method persist because of its potential proarrhythmogenic effect. This is a case describing a 66-year-old Caucasian female with LQTS coexisting with a left bundle branch branch block (LBBB) and an implantable single-cavity cardioverter-defibrillator (ICD VR), who had repeated appropriate high-energy treatments. The upgrade to resynchronisation therapy defibrillator (CRT-D) significantly reduced frequency of ventricular tachycardia and the need for electrical therapies. The normalisation of the left ventricle size, as seen on echo examination, and the improvement of heart failure symptoms were also observed.
长QT综合征（LQTS）的特征是心肌细胞的去极化和复极化紊乱。心脏再同步治疗（CRT）是满足超声心动图和心电图标准的慢性心力衰竭（CHF）患者的重要治疗选择。尽管CRT在10年前就已引入临床实践，但由于其潜在的促心律失常作用，对这种治疗方法的应用仍存在疑虑。这是一例病例，描述了一名66岁的白种女性，患有LQTS并伴有左束支传导阻滞（LBBB）和植入式单腔心脏复律除颤器（ICD VR），她接受了多次适当的高能量治疗。升级为再同步治疗除颤器（CRT-D）显著降低了室性心动过速的频率以及电疗法的需求。超声检查显示左心室大小恢复正常，心力衰竭症状也有所改善。
