King R A, Olds D P, Witkop C J
J Invest Dermatol. 1978 Aug;71(2):136-9. doi: 10.1111/1523-1747.ep12546765.
Human hairbulb tyrosinase from normally pigmented and tyrosinase-positive oculocutaneous albino (TPA) hairbulbs was studied by single hairbulb and by pooled hairbulb assay procedures. The response to temperature and pH was the same for TPA and normal enzyme. The Km for tyrosine as substrate and the Km or dopa as cofactor was the same for TPA and normal enzyme. These studies show that TPA tyrosinase is kinetically normal and that the defect with this form of albinism must be elsewhere in the melanin pathway.
通过单毛囊和合并毛囊检测程序,对来自正常色素沉着且酪氨酸酶阳性的眼皮肤白化病(TPA)毛囊的人毛囊酪氨酸酶进行了研究。TPA酶和正常酶对温度和pH的反应相同。以酪氨酸为底物时的米氏常数(Km)以及以多巴为辅助因子时的Km,TPA酶和正常酶是相同的。这些研究表明,TPA酪氨酸酶在动力学上是正常的,这种白化病形式的缺陷必定存在于黑色素合成途径的其他地方。