Grenoble University Hospital, Department of Maxillo-facial Surgery, Avenue Maquis du Grésivaudan, 38700 La Tronche, France.
Grenoble University Hospital, Department of Pediatric Radiology, Avenue Maquis du Grésivaudan, 38700 La Tronche, France.
J Stomatol Oral Maxillofac Surg. 2017 Oct;118(5):298-301. doi: 10.1016/j.jormas.2017.03.005. Epub 2017 Apr 5.
Nasal glial heterotopia (NGH) is a rare benign tumor of the median line. We describe the case of a child presenting a lateral nasal mass. The characteristics of the prenatal ultrasound and the postnatal clinical examination argued in favor of a congenital hemangioma (CH). The MRI performed at 6 weeks of life suggested glial heterotopia. This diagnosis was confirmed by the pathological analysis. Congenital hemangiomas and nasal glial heterotopies have similar clinical presentations. Prenatal ultrasound diagnosis between NGH and CH is difficult. Fetal MRI is not yet highly specific for these two lesions, but it can eliminate an intracerebral connection in cases of NGH. Postnatal exams are more specific. Flow on the Doppler exam is rapid for CH and slow for NGH. On MRI, these two lesions appear as a hypersignal on T2-weighted sequences, but less intense for NGH than for CH. Distinguishing between NGH and CH can be difficult. This does not have a direct incidence on treatment because it is surgical in both cases.
鼻腔神经胶质异位(NGH)是一种罕见的中线良性肿瘤。我们描述了一例表现为鼻腔外侧肿块的儿童病例。产前超声和产后临床检查的特征提示为先天性血管瘤(CH)。6 周龄时进行的 MRI 检查提示为神经胶质异位。该诊断通过病理分析得到了证实。先天性血管瘤和鼻腔神经胶质异位具有相似的临床表现。NGH 和 CH 之间的产前超声诊断困难。胎儿 MRI 对这两种病变的特异性还不高,但对于 NGH 可以排除颅内连接。产后检查更具特异性。CH 的多普勒检查显示血流较快,而 NGH 较慢。在 MRI 上,这两种病变在 T2 加权序列上呈高信号,但 NGH 比 CH 弱。区分 NGH 和 CH 可能具有一定难度。这不会直接影响治疗,因为两种病变均需手术治疗。