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Congenital factor VII deficiency: Multidisciplinary approach is the key to successful perioperative outcome.

作者信息

Tandale Sushama Raghunath, Khedkar Sunita M, Yadav Aparna Hemraj, Ajatshatru Shivankar

机构信息

Department of Anaesthesia, B J Medical College and Sassoon General Hospital, Pune, Maharashtra, India.

出版信息

Indian J Anaesth. 2017 Mar;61(3):275-276. doi: 10.4103/ija.IJA_2_17.

DOI:10.4103/ija.IJA_2_17
PMID:28405048
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5372415/
Abstract
摘要

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1
Congenital factor VII deficiency: Multidisciplinary approach is the key to successful perioperative outcome.先天性凝血因子VII缺乏症:多学科方法是围手术期取得成功结果的关键。
Indian J Anaesth. 2017 Mar;61(3):275-276. doi: 10.4103/ija.IJA_2_17.
2
Elevated prothrombin time on routine preoperative laboratory results in a healthy infant undergoing craniosynostosis repair: Diagnosis and perioperative management of congenital factor VII deficiency.一名接受颅缝早闭修复术的健康婴儿术前常规实验室检查发现凝血酶原时间延长:先天性因子VII缺乏症的诊断及围手术期管理
Int J Surg Case Rep. 2016;24:77-9. doi: 10.1016/j.ijscr.2016.05.004. Epub 2016 May 6.
3
Kidney Transplant in a Patient With Factor VII Deficiency: Case Report.
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Successful coronary artery bypass graft surgery in severe congenital factor VII deficiency: Perioperative treatment with pd-factor VII concentrate.
Haemophilia. 2019 Mar;25(2):e135-e137. doi: 10.1111/hae.13657. Epub 2018 Dec 27.
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Successful coronary artery bypass graft surgery in severe congenital factor VII deficiency: perioperative treatment with factor VII concentrate.
Thromb Haemost. 2007 Oct;98(4):900-2.
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Surgery in patients with congenital factor VII deficiency - a single center study.先天性因子VII缺乏症患者的手术——一项单中心研究
Pol Przegl Chir. 2018 May 22;90(5):1-5. doi: 10.5604/01.3001.0012.0668.
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Use of recombinant factor VII for tooth extractions in a patient with severe congenital factor VII deficiency: a case report.重组因子VII用于重度先天性因子VII缺乏患者拔牙的病例报告
J Am Dent Assoc. 2015 Apr;146(4):271-5. doi: 10.1016/j.adaj.2014.12.022.
8
Asymptomatic intracranial hemorrhage in a newborn with congenital factor VII deficiency and successful treatment with recombinant activated factor VII.一名患有先天性因子VII缺乏症的新生儿出现无症状颅内出血,经重组活化因子VII成功治疗。
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Uncomplicated stereotactic and open neurosurgical procedures in patients with factor VII deficiency.
Surg Neurol. 1994 Jul;42(1):79-82. doi: 10.1016/0090-3019(94)90255-0.
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[Factor VII deficiency and surgery].
Ann Fr Anesth Reanim. 1999 Aug;18(7):772-5. doi: 10.1016/s0750-7658(00)88455-5.

本文引用的文献

1
Anesthetic management of a patient with factor VII deficiency undergoing laparoscopic colectomy: a case report.一名患有因子VII缺乏症的患者行腹腔镜结肠切除术的麻醉管理:病例报告
JA Clin Rep. 2016;2(1):30. doi: 10.1186/s40981-016-0059-0. Epub 2016 Oct 19.
2
Elevated prothrombin time on routine preoperative laboratory results in a healthy infant undergoing craniosynostosis repair: Diagnosis and perioperative management of congenital factor VII deficiency.一名接受颅缝早闭修复术的健康婴儿术前常规实验室检查发现凝血酶原时间延长:先天性因子VII缺乏症的诊断及围手术期管理
Int J Surg Case Rep. 2016;24:77-9. doi: 10.1016/j.ijscr.2016.05.004. Epub 2016 May 6.
3
rFVIIa administered by continuous infusion during surgery in patients with severe congenital FVII deficiency.手术中持续输注 rFVIIa 治疗严重先天性 FVII 缺乏症患者。
Haemophilia. 2011 Sep;17(5):764-70. doi: 10.1111/j.1365-2516.2011.02596.x. Epub 2011 Jun 26.
4
Factor VII Deficiency: A Rare Case Report.凝血因子 VII 缺乏症:一例罕见病例报告。
Indian J Hematol Blood Transfus. 2010 Jun;26(2):68-9. doi: 10.1007/s12288-010-0023-5. Epub 2010 Oct 6.
5
Clinical picture and treatment strategies in factor VII deficiency.
Haemophilia. 1998 Jul;4(4):689-96. doi: 10.1046/j.1365-2516.1998.440689.x.